Human ALDP / ABCD1

Mouse

Human (tested or 100% immunogen sequence identity)

IgG1 Monoclonal

Unconjugated

Ascites

Unmodified

ALDP1 fragment from aa 279 to 482 as a fusion protein.

aa279-482

Human ALDP. No cross-reactivity with mouse ALDRP, PMP70. Cross-reactivity to an unidentified 80kD MW protein is present in lymphoblastoid cells, but not in several other cells or tissues tested.

• IHC (1:500 - 1:5000)
• ICC (1:500 - 1:5000)
• Western blot (1:500 - 1:5000)
• ELISA (1:500 - 1:5000)

ELISA: 1:500-1:5000. Western Blot: 1:500-1:5000. Immunohistochemistry: 1:500-1:5000. Immunocytochemistry: 1:500-1:5000. Can be used to analyze ALDP protein in cells and tissues from normal individuals, or from patients with adrenoleukodystrophy (ALD) or Zellweger syndrome and related peroxisomal diseases, and provides an excellent marker for peroxisomes (Mosser et al. 1994). About 70% of ALD male patients have no detectable ALDP in fibroblasts or leukocytes. A similar proportion of carrier females may show mosaicism for the presence or absence of ALDP.

Ascites fluid, no preservatives.

Short term: store at 4°C. Long term: store at -20°C. Avoid freeze-thaw cycles.

For research use only. Intended for use by laboratory professionals.

This antibody carries the LSBio 100% Guarantee.

Uniprot: P33897 NCBI: NM_000033 NP_000024.2